Complete list of Publications

Please click HERE or on the link below for a full list of published papers.

Selected Papers


 Steffen J, Vashisht AA, Wan J, Jen JC, Claypool SM, Wohlschlegel JA, Koehler CM. Rapid degradation of mutant SLC25A46 by the ubiquitin-proteasome system results in MFN1/2 mediated hyperfusion of mitochondria. Molecular Biology of the Cell. 2017 Mar 1;28(5):600-612. PMCID: PMC5328619 

 Lu YW, Acoba MG, Selvaraju K, Huang TC, Nirujogi RS, Sathe G, Pandey A, Claypool SMHuman adenine nucleotide translocases physically and functionally interact with respirasomes. Mol Biol Cell. 2017 Apr 12. pii: mbc.E17-03-0195. 


Seifert EL, Gál A, Acoba MG, Li Q, Anderson-Pullinger L, Golenár T, Moffat C, Sondheimer N, Claypool SM, Hajnóczky G. Natural and Induced Mitochondrial Phosphate Carrier Loss: DIFFERENTIAL DEPENDENCE OF MITOCHONDRIAL METABOLISM AND DYNAMICS AND CELL SURVIVAL ON THE EXTENT OF DEPLETION. The Journal of Biological Chemistry. 2016 Dec 9;291(50):26126-26137. PMCID: PMC5207081 

Cole LK, Meija EM, Vandel M, Sparagna GC, Claypool SM, Dyck-Chan L, Klein J, Hatch GM. Impaired Cardiolipin Biosynthesis Prevents Hepatic Steatosis and Diet-Induced Obesity. Diabetes. 2016 Nov;65(11):3289-3300. PMCID: PMC5079636

Lu YW, Galbraith L, Herndon JD, Lu YL, Pras-Raves M, Vervaart M, van Kampen A, Luyf A, Koehler CM, McCaffery JM, Gottlieb E, Vaz FM, Claypool SM. Defining functional classes of Barth syndrome mutation in humans. Human Molecular Genetics. 2016 May 1;25(9):1754-70. PMCID: PMC4986330 

Calzada E, Onguka O, Claypool SM. Phosphatidylethanolamine Metabolism in Health and Disease. International Review of Cell and Molecular Biology. 2016;321:29-88. PMCID: PMC4778737 

Pokorná L, Čermáková P, Horváth A, Baile MG, Claypool SM, Griač P, Malínský J, Balážová M. Specific degradation of phosphatidylglycerol is necessary for proper mitochondrial morphology and function. Biochimica et Biophysica Acta (BBA) - Bioenergetics, 2016 Jan;1857(1):34-45. PMCID: PMC4690203 


Bohovych I, Fernandez MR, Rahn JJ, Stackley KD, Bestman JE, Anandhan A, Franco R, Claypool SM, Lewis RE, Chan SS, Khalimonchuk O. Metalloprotease OMA1 Fine-tunes Mitochondrial Bioenergetic Function and Respiratory Supercomplex Stability. Scientific Reports. 2015 Sep 14;5:13989. PMCID: PMC4568518 

Onguka O, Calzada E, Ogunbona OB, Claypool SM. Phosphatidylserine Decarboxylase 1 Autocatalysis and Function Does Not Require a Mitochondrial-specific Factor. The Journal of Biological Chemistry, 2015 May 15;290(20):12744-52. PMCID: PMC4432291 

Lu YW, Claypool SM. Disorders of phospholipid metabolism: an emerging class of mitochondrial disease due to defects in nuclear genes. Frontiers in Genetics, 2015 Feb 3;6:3. doi: 10.3389/fgene.2015.00003. PMCID: PMC4315098 

Xu Y, Malhotra A, Claypool SM, Ren M, Schlame M. Tafazzins from Drosophila and mammalian cells assemble in large protein complexes with a short half-life. Mitochondrion, 2015 Jan 15;21C:27-32. PMCID: PMC4693151